ESPN 51th Annual Meeting

ESPN 2018


 
Multicystic dysplastic Kidney : about 54 cases
ABIR BOUSSETTA ONS NAIJA YOSRA HAMMI MERIEM FERJANI BOUBAKR LEGSIR YOUSSEF GHARBI TAHER GARGAH NEJIB KAABAR

 
Introduction:

 

Multicystic dysplastic disease (MCK) is a dysembryoplasia resulting in a non-functioning kidney, its incidence is 1/4300 live births. Usually unilateral, it affects mostly boys with left sided predominance. In 7 to 80% it is associated with urogenital or remote anomalies. Through a study of 54 cases of multicystic dysplastic kidney (MCK), we looked after the diagnostic, therapeutic and evolutionary characteristics of this illness.

Material and methods:

 

This is a retrospective study of 54 consecutive of MCK collected in 13 years (2004-2017).

Results:

 

In 35% of cases, MCK was diagnosed by prenatal ultrasound. Postnatal diagnosis was suggested following urinary tract infections (15 cases), hypertension (6 cases), lumber mass (3 cases), renal failure (2 cases) and often fortuitously (4 cases). Clinical examination revealed a urogenital malformation (5 cases), a lumber mass (4 cases), a lumber pain (2 cases) and a collateral venous circulation (1 case). In all cases, diagnosis was confirmed by ultrasound. Scintigraphy showed non-functional parenchyma in 34 cases. voiding cystourethrography notes vesicoureteral reflux in 14 patients. Fifty patients undergone surgery and 2 were conservatively treated with good evolution. Two patients had bilateral but partial dysplasia, one is at end stage renal failure, the other is dead. A third patient with multiple malformations dead at H16 of life.

Conclusions:

 

MCK is a relatively common pathology in children, accompanied by urogenital or remote abnormalities which can condition the prognosis in many cases. The current attitude is non-operative but some conditions can oblige to the operative choice. Whatever the attitude, a long-term follow-up, with some precautions is necessary to evaluate the remaining kidney’s function.